has material basis in autosomal recessive disease proteosome-associated autoinflammatory syndrome proteosome-associated autoinflammatory syndrome 4 DOID:0060915 MIM:619183 A proteasome-associated autoinflammatory syndrome that is characterized by onset of panniculitis and erythematous skin lesions in early infancy with variable features of lymphadenopathy, myositis, delayed motor and speech development and autoimmune features and that has_material_basis_in compound heterozygous mutation in the PSMG2 gene on chromosome 18p11. PRAAS4 disease_ontology autosomal recessive inheritance