DO_rare_slim NCIthesaurus primary cutaneous T-cell non-Hodgkin lymphoma subcutaneous panniculitis-like T-cell lymphoma UMLS_CUI:C0522624 SNOMEDCT_US_2025_09_01:404133000 NCI:C6918 ORDO:86884 MESH:C537503 ICD10CM:C86.3 ORDO:86884 MIM:618398 DOID:0070662 MIM:618398 MESH:C537503 disease_ontology ICD10CM:C86.3 A primary cutaneous T-cell non-Hodgkin lymphoma characterized by infiltration of subcutaneous tissue by neoplastic alpha-beta cytotoxic T cells mimicking panniculitis. Homozygous or compound heterozygous mutation in the HAVCR2 gene may contribute to development of this disease, with some evidence of incomplete penetrance. NCI:C6918 ICDO:9708/3 SPTCL UMLS_CUI:C0522624 ICDO:9708/3