histiocytic and dendritic cell neoplasm histiocytic sarcoma https://www.malacards.org/card/histiocytic_sarcoma ICD10CM:C96.A ICD9:171.9 icd11.foundation:911785965 icd11.foundation:1925254893 histiocytic sarcoma Orphanet:86896 sarcoma, histiocytic, malignant UMLS:C0334663 MONDO:0019479 SCTID:109988003 HS MESH:D054747 MEDGEN:137793 ONCOTREE:HS ICDO:9755/3 An aggressive malignant neoplasm with a poor response to therapy, usually presenting as stage III/IV disease. It is characterized by the presence of neoplastic cells with morphologic and immunophenotypic characteristics similar to those seen in mature histiocytes. DOID:0080915 GARD:0019080 NCIT:C27349