obsolete_Pleuropulmonary blastoma true UMLS:C1266144 3.88.0 Orphanet:64742 MedDRA:10080682 Pleuropulmonary blastoma (PPB) is a rare pediatric tumor of the lung that arises during fetal lung development and is often part of an inherited cancer syndrome (Hill et al., 2009). PPBs contain both epithelial and mesenchymal cells. Early in tumorigenesis, cysts form in lung airspaces, and these cysts are lined with benign-appearing epithelium. Hannah McLaren OMIM:601200 Replaced by Mondo term MONDO_0011014, with which this term was previously merged. Use: http://purl.obolibrary.org/obo/MONDO_0011014 http://purl.obolibrary.org/obo/MONDO_0011014 MESH:C537516