obsolete_PEComa true Replaced by Mondo term MONDO_0006359, with which this term was previously merged. Use: http://purl.obolibrary.org/obo/MONDO_0006359 ONCOTREE:PECOMA MESH:D054973 DOID:2643 tumor with perivascular epithelioid cell differentiation 3.88.0 EFO:1000464 NCIT:C38150 MeSH defintion: A family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. These cells do not have a normal anatomic homolog. (From Fletcher CDM, et. al., World Health Organization Classification of Tumors: Pathology and Genetics of Tumors of Soft Tissue and Bone, 2002). PEComa A soft tissue neoplasm composed of perivascular epithelioid cells. Representative examples include angiomyolipoma, clear cell-sugar-tumor of the lung, and lymphangioleiomyomatosis. perivascular epithelioid cell tumor neoplasm with perivascular epithelioid cell differentiation http://purl.obolibrary.org/obo/MONDO_0006359 UMLS:C1300127