Syndrome associated with hypertrophic cardiomyopathy Progressive sensorineural hearing loss - hypertrophic cardiomyopathy orphanet Progressive sensorineural hearing loss - hypertrophic cardiomyopathy is an extremely rare disorder described in one family to date that is characterized by progressive, late onset, autosomal dominant sensorineural hearing loss, QT interval prolongation, and mild cardiac hypertrophy. OMIM:606346 Progressive neurosensory hearing loss - hypertrophic cardiomyopathy Progressive neurosensory deafness - hypertrophic cardiomyopathy Progressive sensorineural deafness - hypertrophic cardiomyopathy Syndromic genetic deafness