obsolete_Classic Mayer-Rokitansky-Küster-Hauser syndrome true Mayer-Rokitansky-Küster-Hauser syndrome type 1 ICD10:Q51.8 3.41.0 Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome type 1 is the classic type of MRKH syndrome (see this term) characterized by an isolated form of congenital aplasia of the uterus and upper two thirds of the vagina in otherwise phenotypically normal females. Replaced with Mondo term. orphanet http://purl.obolibrary.org/obo/MONDO_0010173 Rokitansky sequence Classic Rokitansky syndrome MRKH syndrome type 1 OMIM:277000 Classic MRKH syndrome