Autosomal dominant limb-girdle muscular dystrophy Neuromuscular disease with dilated cardiomyopathy Autosomal dominant limb-girdle muscular dystrophy type 1B Autosomal dominant limb-girdle muscular dystrophy type 1B (LGMD1B) is a limb girdle muscular dystrophy (LMGD; see this term)a laminopathy, characterized by progressive limb girdle weakness, usually affecting the pelvic girdle before humeral muscles, mild jointoint contractures, age-related atrioventricular cardiac conduction disturbances and dilated cardiomyopathyinvolvement is frequently associated. LGMD1B orphanet ICD10:G71.0 Limb-girdle muscular dystrophy due to lamin A/C deficiency OMIM:159001