Rare genetic diabetes mellitus MODY OMIM:612225 OMIM:616329 OMIM:606391 ICD10:E11.8 MODY (maturity-onset diabetes of the young) is a rare, familial, clinically and genetically heterogeneous form of diabetes characterized by young age of onset (generally 10-45 years of age) with maintenance of endogenous insulin production, lack of pancreatic beta-cell autoimmunity, absence of obesity and insulin resistance and extra-pancreatic manifestations in some subtypes. OMIM:616511 OMIM:613375 OMIM:125850 OMIM:610508 OMIM:613370 OMIM:609812 orphanet OMIM:600496 OMIM:125851 OMIM:606394 Maturity onset diabetes of the young (MODY) MODY is a rare form of diabetes which is different from both Type 1 and Type 2 diabetes, and runs strongly in families. MODY is caused by a mutation (or change) in a single gene. (https://www.diabetes.org.uk/Diabetes-the-basics/Other-types-of-diabetes/MODY/) OMIM:606392 Maturity-onset diabetes of the young