lymphadenitis Kawasaki disease ICD10CM:M30.3 UMLS:C0026691 DOID:13378 NCIT:C34825 SCTID:75053002 ICD9:446.1 EFO:0004246 icd11.foundation:540285662 acute febrile mucocutaneous lymph node syndrome [MCLS] Kawasaki syndrome mucocutaneous lymph node syndrome MESH:D009080 MEDGEN:10118 Orphanet:2331 OMIM:611775 A rare inflammatory disease characterized by an acute febrile, systemic, self-limiting, medium-vessel vasculitis primarily affecting children. It often causes acute coronary arteritis which is associated with coronary arterial aneurysms (CAA) that may be life threatening when untreated. infantile polyarteritis nodosa GARD:0006816 acute febrile mucocutaneous lymph node syndrome MedDRA:10023320 vasculitis