PathwayStep1433 PathwayStep1437 PathwayStep1426 PathwayStep1419 PathwayStep1407 NADPH regeneration Beta-oxidation of very long chain fatty acids Plasmalogen biosynthesis Alpha-oxidation of phytanate Beta-oxidation of pristanoyl-CoA Peroxisomal lipid metabolism Authored: D'Eustachio, P, 2009-02-11 15:12:47 Edited: D'Eustachio, P, 2009-02-11 15:12:47 GENE ONTOLOGYGO:0044255 In humans, the catabolism of phytanate, pristanate, and very long chain fatty acids as well as the first four steps of the biosynthesis of plasmalogens are catalyzed by peroxisomal enzymes. Defects in any of these enzymes or in the assembly of peroxisomes are associated with severe developmental disorders (Wanders and Watherham 2006). Pubmed16756494 Reactome Database ID Release 43390918 Reactome, http://www.reactome.org ReactomeREACT_16957 Reviewed: Jassal, B, 2009-02-27 15:21:18