has role valeric acid 4-methyl-2-oxopentanoate branched-chain keto acid 2-oxo monocarboxylic acid 4-methyl-2-oxopentanoic acid CHEBI:48430 CHEBI:1891 alpha-ketoisocaproic acid 2-Oxoisocaproate 2-OXO-4-METHYLPENTANOIC ACID PDBeChem:COI CHEBI:41619 4-Methyl-2-oxopentanoate 4-methyl-2-oxovaleric acid MetaCyc:2K-4CH3-PENTANOATE A 2-oxo monocarboxylic acid that is pentanoic acid (valeric acid) substituted with a keto group at C-2 and a methyl group at C-4. A metabolite that has been found to accumulate in maple syrup urine disease. 4-methyl-2-oxopentanoic acid HMDB:HMDB0000695 DrugBank:DB03229 KNApSAcK:C00019677 Ketoleucine KEGG:C00233 human metabolite algal metabolite