Multiple pulmonary cysts Congenital pulmonary airway malformation 2011-01-18T11:56:02Z CCAM SNOMEDCT_US:111318005 HP:0006545 Cystic adenomatoid lung disease Congenital pulmonary airway malformation (CPAM) - previously known as congenital cystic adenomatoid malformation (CCAM) - is a relatively rare developmental malformation of the lower respiratory tract. It is a hamartomatous, dysplastic developmental abnormality of the lung characterized by abnormal airway patterning during lung branching morphogenesis and is formed by abnormal branching of the immature bronchioles. HP:0006540 Congenital cystic adenomatoid malformation HP:0010959 Congenital cystic disease of the lung Congenital cystic adenomatoid malformation of the lung The term CPAM has been recommended as being preferable to the term congenital cystic adenomatoid malformation, since the lesions are cystic or adenomatoid in only a limited number of cases. Only three types of CPAMs are distinguished at imaging: large cyst CPAM (type I) and small cyst CPAM (type II), which constitute macrocystic CPAMs; and microcystic or solid type (type III) lesions, which have cysts that are smaller than 5 mm in diameter, with no discernible cystic spaces. UMLS:C0010668 Abnormal fetal pulmonary morphology