Abnormality of the periorbital region Bitemporal forceps marks 2012-02-25T05:25:36Z Focal facial dermal dysplasia Congenital, bilateral, scarlike facial lesions Congenital, bilateral, scarlike facial lesions have been reported under several titles, such as hereditary symmetric systemic aplastic nevi, congenital ectodermal dysplasia of the face, familial focal facial dermal dysplasia, bitemporal aplasia cutis congenita, and focal facial dermal dysplasia (FFDD). The findings are congenital, bilateral scarlike facial lesions in the preauricular or cheek areas. The lesions may present as slightly depressed hypopigmented scarlike oval plaques measuring about 1 cm and may have a surrounding rim of fine lanugo-like hair. Skin biopsy can reveal an atrophic epidermis with a thinned dermis devoid of adnexal structures. Elastic fibers are absent in the affected areas, as can be shown by Verhoeff-van Giesen staining. Bilateral temporal scarlike defects, which are said to resemble forceps marks. HP:0011336 Bitemporal aplasia cutis congenita UMLS:C4020754 Congenital ectodermal dysplasia of the face Temporal skin defect UMLS:C4023409