Transposition of the great arteries Abnormal spatial orientation of the cardiac segments Levotransposition of the great arteries 2012-04-07T10:48:56Z Congenitally corrected transposition of the great arteries L-transposition of the great arteries SNOMEDCT_US:83799000 HP:0011540 ccTGA L-TGA HP:0011605 Congenitally corrected TGA cTGV EPCC:01.01.03 Atrioventricular and ventriculo-arterial discordance Congenitally corrected transposition of the great arteries (ccTGA) is a discordance of atrioventricular (AV) and ventriculoarterial connections. The anatomy of ccTGA involves systemic venous drainage to the morphologic right atrium (mRA), which is connected via the mitral valve to the morphologic left ventricle (mLV) whose outflow is the pulmonary arterial system. The pulmonary venous drainage arrives at the morphologic left atrium (mLA), which crosses the tricuspid valve into the morphologic right ventricle (mRV) with outflow into the systemic arterial system. In isolation, ccTGA has an in-series circulation without mixing; therefore, the presence or absence of associated defects dictates the patient's clinical presentation. HP:0031349 cTGA Ventricular inversion Physiologically corrected transposition of the great vessels L-transposition SNOMEDCT_US:56743000 UMLS:C0344616 UMLS:C0232301 ccTGV ICD-10:Q20.5 Discordant atrioventricular a ventriculo-arterial connections