Congenital malformation of the right heart Uhl's anomaly 2012-04-11T08:59:07Z HP:0011724 Uhl anomaly of the right ventricle refers to the almost complete absence of right ventricular myocardium, normal tricuspid valve, and preserved septal and left ventricular myocardium. SNOMEDCT_US:2829000 UMLS:C0265857