Lymphatic vessel neoplasm Pulmonary lymphangiomyomatosis 2014-05-24T05:00:46Z Lymphangioleiomyomatosis HP:0012798 UMLS:C0751674 UMLS:C0238399 Pulmonary myomatosis Pulmonary lymphangiomyomatosis is a manifestation of lymphangioleiomyomatosis, which may also affect extrapulmonary locations. It can be seen in tuberous sclerosis. SNOMEDCT_US:73017001 Infiltration of smooth muscle-like cells in lymph vessels as well as the lung (pleura, alveolar septa, bronchi, pulmonary vessels and lymphatics as well as lymph nodes, especially in posterior mediastinum and retroperitoneum). Focal emphysema can develop because of airway narrowing, and the thoracic duct may be obliterated. Pulmonary lymphangiomyomatosis may lead to multiple small cysts with a hamartomatous proliferation of smooth muscle in their walls. Neoplasm of the lung