Potter sequence A rare, lethal congenital malformation characterized by bilateral renal agenesis and the absence or decreased volume of amniotic fluid (oligohydramnios). The presence of oligohydramnios gives rise to congenital anomalies that include hypoplastic lungs, lower extremities abnormalities, and characteristic facial features (low-set ears, widely separated eyes, nose flattening, and receding chin). Newborn infants usually die of respiratory failure. DOID:12594 Editor note: check for subtypes, relationship to OMIM:263200 GARD:0004462 ICD10:Q60.6 MONDO:0001558 NCIT:C40435 Potter syndrome Potter's sequence Potter's syndrome SCTID:41962002 UMLS:C0178426 oligohydramnios sequence syndromic disease oligohydramnios (disease)