rhabdoid tumor An aggressive malignant embryonal neoplasm usually occurring during childhood. It is characterized by the presence of large cells with abundant cytoplasm, large eccentric nucleus, and a prominent nucleolus and it is associated with abnormalities of chromosome 22. It can arise from the central nervous system, kidney, and the soft tissues. The prognosis is poor. DOID:3672 EFO:0005701 GARD:0007572 ICD10:C49.9 ICDO:8963/3 MESH:D018335 MONDO:0002728 NCIT:C3808 ONCOTREE:MRT Orphanet:69077 UMLS:C0206743 malignant rhabdoid tumor malignant rhabdoid tumour rhabdoid cancer rhabdoid sarcoma rhabdoid tumor embryonal neoplasm soft tissue sarcoma