has modifier hereditary Wilms tumor DOID:5183 Familial embryonal neoplasm derived from nephrogenic blastemal cells. Several lines of differentiation, including blastemal, stromal and epithelial, are usually expressed. Comprises approximately 1% of Wilms tumors. (AFIP fascicle version 2.0) MONDO:0003321 NCIT:C8496 OMIMPS:194070 UMLS:C0677779 WT1 familial Wilms tumor familial Wilms' tumor hereditary Wilms tumor hereditary Wilms' tumor hereditary kidney adenosarcoma hereditary nephroblastoma hereditary renal adenosarcoma Mendelian disease Wilms tumor kidney Wilms tumor inherited