disease has location clear cell sarcoma kidney sarcoma clear cell sarcoma of kidney A rare pediatric sarcoma affecting the kidney. It is characterized by the presence of epithelioid or spindle cells forming cords or nests, separated by fibrovascular septa. It is associated with internal tandem duplications in the BCOR gene. It metastasizes to lung, bone, brain and soft tissue. CCSK DOID:4880 EFO:0000350 ICD10:C64 ICDO:8964/3 MONDO:0005006 NCIT:C4264 ONCOTREE:CCSK Orphanet:457246 UMLS:C0334488 UMLS:CN242113 childhood clear cell sarcoma of the kidney childhood kidney clear cell sarcoma childhood renal clear cell sarcoma clear cell sarcoma - kidney clear cell sarcoma of kidney clear cell sarcoma of the kidney kidney clear cell sarcoma pediatric kidney clear cell sarcoma pediatric renal clear cell sarcoma renal clear cell sarcoma kidney