pericytic neoplasm neoplasm with perivascular epithelioid cell differentiation A soft tissue neoplasm composed of perivascular epithelioid cells. Representative examples include angiomyolipoma, clear cell-sugar-tumor of the lung, and lymphangioleiomyomatosis. DOID:2643 EFO:1000464 MESH:D054973 MONDO:0006359 MeSH defintion: A family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. These cells do not have a normal anatomic homolog. (From Fletcher CDM, et. al., World Health Organization Classification of Tumors: Pathology and Genetics of Tumors of Soft Tissue and Bone, 2002). NCIT:C38150 ONCOTREE:PECOMA PEComa UMLS:C1300127 neoplasm with perivascular epithelioid cell differentiation perivascular epithelioid cell tumor tumor with perivascular epithelioid cell differentiation soft tissue neoplasm