disease has basis in dysfunction of CYP11B1 glucocorticoid-remediable aldosteronism ACTH-dependent hyperaldosteronism syndrome DOID:14080 FH 1 FH-I FH1 Familial hyperaldosteronism type I (FH-I) is a rare heritable, glucocorticoid remediable form of primary aldosteronism (PA) characterized by early-onset hypertension, hyperaldosteronism, variable hypokalemia, low plasma renin activity (PRA), and abnormal production of 18-oxocortisol and 18-hydroxycortisol. GARD:0002790 GRA HALD1 ICD10:E26.0 ICD10:E26.02 ICD9:255.11 MESH:C563177 MONDO:0007080 OMIM:103900 Orphanet:403 UMLS:C1260386 UMLS:C3838731 aldosteronism, sensitive to dexamethasone dexamethasone sensitive hypertension dexamethasone-sensitive hypertension familial hyperaldosteronism type 1 familial hyperaldosteronism type I glucocorticoid sensitive hypertension glucocorticoid-remediable aldosteronism glucocorticoid-sensitive hypertension glucocorticoid-suppressible hyperaldosteronism https://rarediseases.info.nih.gov/diseases/2790/glucocorticoid-remediable-aldosteronism hyperaldosteronism, familial type 1 hyperaldosteronism, familial, type 1 hyperaldosteronism, familial, type I genetic hypertension familial hyperaldosteronism