disease has basis in dysfunction of disease has location AVP autosomal dominant disease pituitary gland disease diabetes insipidus neurohypophyseal diabetes insipidus ADH deficiency AVP deficiency Arginine vasopressin deficiency DOID:12388 Hereditary central diabetes insipidus is a rare genetic subtype of central diabetes insipidus (CDI) characterized by polyuria and polydipsia due to a deficiency in vasopressin (AVP) synthesis. ICD10:E23.2 MONDO:0007450 NCIT:C84933 OMIM:125700 Orphanet:30925 SCTID:45369008 antidiuretic hormone deficiency central diabetes insipidus diabetes insipidus of pituitary gland diabetes insipidus, cranial type diabetes insipidus, neurohypophyseal diabetes insipidus, primary central hereditary CDI hereditary central diabetes insipidus hereditary neurogenic diabetes insipidus neurogenic diabetes insipidus pituitary diabetes insipidus pituitary gland diabetes insipidus vasopressin defective diabetes insipidus vasopressin deficiency central diabetes insipidus genetic nervous system disorder pituitary gland