disease has basis in dysfunction of HNF1B renal cysts and diabetes syndrome CAKUT with diabetes DOID:0111101 FJHN atypical FJHN, atypical GARD:0010221 HNF1B-MODY HNF1B-related renal cysts and diabetes syndrome ICD10:E11.2 MESH:C535520 MODY type 5 MODY5 MONDO:0007669 NCIT:C123018 OMIM:137920 Orphanet:93111 RCAD RCAD syndrome Renal cysts and diabetes syndrome (RCAD) is a rare form of maturity-onset diabetes of the young (MODY) characterized clinically by heterogeneous cystic renal disease and early-onset familial non-autoimmune diabetes. Pancreatic atrophy, liver dysfunction and genital tract anomalies are also features of the syndrome. SCTID:446641003 UMLS:C0431693 UMLS:CN206512 atypical FJHN atypical familial juvenile hyperuricemic nephropathy congenital anomalies of the kidney and urinary tract with diabetes familial hypoplastic glomerulocystic kidney glomerulocystic kidney disease, hypoplastic type glomerulocystic kidney, familial hypoplastic hepatocyte nuclear Factor 1-beta-associated monogenic diabetes https://rarediseases.info.nih.gov/diseases/10221/maturity-onset-diabetes-of-the-young-type-5 hyperuricemic nephropathy, familial juvenile, atypical hypoplastic type glomerulocystic kidney disease maturity onset diabetes of the Young, type 5 maturity-onset diabetes of the Young, type 5 maturity-onset diabetes of the young type 5 renal cysts and diabetes syndrome renal cysts-maturity-onset diabetes of the young syndrome renal dysfunction-early-onset diabetes syndrome developmental anomaly of metabolic origin syndromic urogenital tract malformation maturity-onset diabetes of the young (disease) syndromic renal or urinary tract malformation