Mendelian disease fibronectin glomerulopathy DC:0000174 Editor note: consider splitting out type 1, and also separate class for giant subtype Fibronectin glomerulopathy is a hereditary kidney disease characterized by proteinuria, type IV renal tubular acidosis, microscopic hematuria and hypertension that may lead to end-stage renal failure in the second to sixth decade of life. GARD:0009268 GFND GFND1 GFND2 ICD10:N07.6 MESH:C536826 MESH:C562900 MONDO:0007671 OMIMPS:137950 Orphanet:84090 SCTID:236535001 fibronectin glomerulopathy glomerular nephritis, familial, with fibronectin deposits glomerulopathy with fibronectin deposits glomerulopathy with fibronectin deposits 1 glomerulopathy with fibronectin deposits 2 glomerulopathy with giant fibrillar deposits https://rarediseases.info.nih.gov/diseases/9268/glomerulopathy-with-fibronectin-deposits-1 lobular glomerulopathy, familial primary glomerular disease