disease has basis in dysfunction of disease has feature WT1 Male pseudohermaphroditism Diffuse mesangial sclerosis autosomal dominant disease Denys-Drash syndrome DDS DOID:3764 Denys Drash syndrome Denys-Drash syndrome Denys-Drash syndrome (DDS) is a rare urogenital disorder characterized by the association of diffuse mesangial sclerosis (DMS), male pseudohermaphroditism with a 46,XY karyotype, and nephroblastoma. Drash syndrome GARD:0005576 ICD10:N04.1 ICD9:189.0 MESH:D030321 MONDO:0008682 MedDRA:10070179 NCIT:C84668 OMIM:194080 Orphanet:220 SCTID:236385009 UMLS:C0950121 UMLS:C3151568 Wilms tumor and pseudo- or true hermaphroditism Wilms tumor and pseudohermaphroditism nephropathy associated with male pseudohermaphroditism and Wilms' tumor nephropathy, Wilms tumor, and genital anomalies nephrotic syndrome type 4 pseudohermaphroditism, nephron disorder and Wilms' tumor primary glomerular disease polymalformative genetic syndrome with increased risk of developing cancer syndrome with 46,XY disorder of sex development