disease has basis in dysfunction of EIF2AK4 pulmonary venoocclusive disease 2 A rare form of pulmonary arterial hypertension (PAH) characterized by a capillary infiltration of the pulmonary interstitium, bronchioles and pleura leading to elevated pulmonary arterial resistance and right heart failure. PCH is potentially fatal. Editor note: check ORDO class - not clear if it intends to be the same as PVOD2 GARD:0008527 ICD10:D18.0 ICD9:416.8 MESH:C535861 MONDO:0009329 OMIM:234810 Orphanet:199241 PVOD2 SCTID:233949008 UMLS:C0340548 familial pulmonary capillary hemangiomatosis hemangiomatosis, familial pulmonary capillary pulmonary capillary hemangiomatosis pulmonary venoocclusive disease 2, autosomal recessive pulmonary venoocclusive disease