disease has basis in dysfunction of disease has feature ATP6V1B1 Sensorineural hearing impairment renal tubular acidosis, distal, 2, with progressive sensorineural hearing loss AR dRTA with hearing loss AR dRTA wth deafness GARD:0004666 ICD9:389.8 ICD9:588.89 MESH:C562897 MONDO:0009968 OMIM:267300 Orphanet:93611 RTA with progressive nerve deafness SCTID:236532003 SCTID:722468005 UMLS:C0403554 UMLS:C4302514 autosomal recessive distal renal tubular acidosis with deafness autosomal recessive distal renal tubular acidosis with hearing loss distal renal tubular acidosis co-occurrent with sensorineural deafness renal tubular acidosis progressive nerve deafness renal tubular acidosis type 1b renal tubular acidosis with deafness renal tubular acidosis with progressive nerve deafness renal tubular acidosis, autosomal recessive, with progressive nerve deafness renal tubular acidosis, distal, with progressive nerve deafness autosomal recessive distal renal tubular acidosis