disease has basis in dysfunction of DGKE familial nephrotic syndrome hereditary nephritis immunoglobulin-mediated membranoproliferative glomerulonephritis Ahus, susceptibility to, 7 Glomerulonephritis characterized by mesangial proliferation, endocapillary proliferation, and glomerular capillary wall remodeling with immune complex deposits from classical complement pathway activation. ICD10:N00.5 Ig-mediated MPGN Ig-mediated membranoproliferative glomerulonephritis Immunoglobulin-mediated MPGN MONDO:0014005 Mesangiocapillary glomerulonephritis type 1 NCIT:C123055 NPHS7 OMIM:615008 Orphanet:329903 hemolytic uremic syndrome, atypical, susceptibility to, 7 immune Complex mediated membranoproliferative glomerulonephritis membranoproliferative glomerulonephritis type I nephrotic syndrome, type 7 nephrotic syndrome, type 7, with membranoproliferative glomerulonephritis atypical hemolytic-uremic syndrome primary membranoproliferative glomerulonephritis