has modifier pulmonary hypertension pulmonary arterial hypertension GARD:0007501 MONDO:0015924 MedDRA:10064911 Orphanet:182090 PAH PPH Pulmonary arterial hypertension (PAH) is a group of diseases characterized by elevated pulmonary arterial resistance leading to right heart failure. PAH is progressive and potentially fatal. PAH may be idiopathic and/ or familial, or induced by drug or toxin (drug-or toxin-induced PAH) or associated with other diseases like congenital heart disease, connective tissue disease, HIV, schistosomiasis, portal hypertension (PAH associated with other disease). SCTID:11399002 UMLS:C2973725 UMLS:CN200519 idiopathic pulmonary hypertension rare