bilateral renal agenesis Bilateral renal agenesis is the most profound form of renal agenesis, characterized by complete absence of kidney development, absent ureters and subsequent absence of fetal renal function resulting in Potter sequence with pulmonary hypoplasia related to oligohydramnios, which is fatal shortly after birth. DOID:0080200 ICD10:Q60.1 MONDO:0015986 NCIT:C101219 Orphanet:1848 bilateral renal aplasia renal agenesis, bilateral renal agenesis (disease)