has modifier Autosomal recessive inheritance autosomal recessive disease distal renal tubular acidosis (disease) autosomal recessive distal renal tubular acidosis AR dRTA Autosomal recessive distal renal tubular acidosis (AR dRTA) is an inherited form of distal renal tubular acidosis (dRTA) characterized by hypokalemic hyperchloremic metabolic acidosis. Deafness often occurs either early or later on in life but may be absent or never be diagnosed. ICD10:N25.8 MONDO:0018440 Orphanet:402041 UMLS:C1864498 autosomal recessive distal RTA autosomal recessive distal renal tubular acidosis (disease) distal renal tubular acidosis (disease), autosomal recessive syndromic genetic deafness