has modifier hereditary renal cell carcinoma clear cell renal carcinoma inherited renal cancer-predisposing syndrome hereditary clear cell renal cell carcinoma A manifestation of von Hippel-Lindau disease or other familial renal cell cancer syndromes that present as a malignant epithelial neoplasm of the kidney. It is characterized by the presence of lipid-containing clear cells within a vascular network. The tumor usually is bilateral and polycentric, and metastasizes to unusual sites. Late metastasis is common. DOID:7192 Hereditary clear cell renal cell cancer ICD10:C64 MONDO:0004137 MONDO:0018492 NCIT:C36260 Orphanet:422526 SCTID:764961009 UMLS:CN237493 hereditary clear cell renal carcinoma hereditary clear cell renal cell adenocarcinoma hereditary clear cell renal cell carcinoma hereditary conventional (clear cell) renal cell carcinoma hereditary conventional renal cell carcinoma inherited