rare diabetes mellitus type 2 maturity-onset diabetes of the young (disease) DOID:0050524 GARD:0003697 HP:0004904 ICD10:E11.8 ICD10:E11.9 KEGG:04950 MESH:C562772 MODY MODY (maturity-onset diabetes of the young) is a rare, familial, clinically and genetically heterogeneous form of diabetes characterized by young age of onset (generally 10-45 years of age) with maintenance of endogenous insulin production, lack of pancreatic beta-cell autoimmunity, absence of obesity and insulin resistance and extra-pancreatic manifestations in some subtypes. MONDO:0018911 Mason type diabetes Mason-type diabetes NCIT:C114769 OMIM:606391 Orphanet:552 SCTID:609561005 UMLS:C0342276 maturity onset diabetes of the young maturity-onset diabetes of the young