has modifier familial nephrotic syndrome idiopathic nephrotic syndrome familial idiopathic steroid-resistant nephrotic syndrome Familial idiopathic steroid-resistant nephrotic syndrome is characterized by a nephrotic syndrome with often early onset. ICD10:N04.1 ICD10:N04.3 ICD10:N04.8 MONDO:0019006 Orphanet:656 SCTID:718141008 UMLS:C1868672 UMLS:C4273714 UMLS:CN536255 familial idiopathic nephrotic syndrome inherited steroid-resistant nephrotic syndrome