collagen type III glomerulopathy Collagen type III glomerulopathy is a rare glomerular disease characterized by abnormal accumulation of type III collagen within the mesangium and subendothelial space of the glomerulus. Clinically it usually manifests with proteinuria (often in the nephrotic range), microscopic hematuria, peripheral edema and/or hypertension. In some cases progression to end-stage renal failure is observed. Collagenofibrotic glomerulopathy ICD10:N07.6 ICD9:583.89 MONDO:0019396 Orphanet:84087 SCTID:708127008 UMLS:C3872695 UMLS:CN206095 secondary glomerular disease