primary congenital glaucoma Primary congenital glaucoma (PCG) is characterized by elevated intraocular pressure (IOP), enlargement of the globe (buphthalmos), edema, and opacification of the cornea with rupture of Descemet's membrane (Haab's striae), thinning of the anterior sclera and iris atrophy, anomalously deep anterior chamber, and structurally normal posterior segment except for progressive glaucomatous optic atrophy. Symptoms include photophobia, blepharospasm, and excessive tearing. Typically, the diagnosis is made in the first year of life. Depending on when treatment is instituted, visual acuity may be reduced and/or visual fields may be restricted. In untreated individuals, blindness invariably occurs. primary congenital glaucoma DOID:0050593 primary congenital glaucoma (disease) SCTID:415176004 UMLS:C1533041 MONDO:0000365 GARD:0022755 primary congenital glaucoma (disease) MEDGEN:288550 icd11.foundation:517092878 HP:0008007 NCIT:C150251 congenital glaucoma