chronic pulmonary heart disease idiopathic pulmonary arterial hypertension https://github.com/monarch-initiative/mondo/issues/9097 https://github.com/monarch-initiative/mondo/issues/9136 https://www.malacards.org/card/primary_pulmonary_hypertension ICD10CM:I27.0 ICD9:416.0 SCTID:697898008 primary pulmonary hypertension DOID:14557 Orphanet:275766 Previously referred to as primary pulmonary hypertension, idiopathic PAH meets the hemodynamic criteria for PAH but is not associated with another disease process. PMID:35412560 IPAH MONDO:0001999 icd11.foundation:265520344 UMLS:C3203102 primary pulmonary arterial hypertension MEDGEN:468368 idiopathic pulmonary arterial hypertension A sporadic form of pulmonary arterial hypertension (PAH) characterized by elevated pulmonary arterial resistance leading to right heart failure. IPAH is progressive and potentially fatal and not associated with an underlying condition or family history of PAH. The etiology is unknown. GARD:0027594 MedDRA:10065151 pulmonary arterial hypertension idiopathic disease