neurofibrosarcoma https://github.com/monarch-initiative/mondo/issues/8583 https://www.malacards.org/card/neurofibrosarcoma A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with neurofibromatosis 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72) MEDGEN:104927 2025-04-01 neurosarcoma [obs] MONDO:0002675 UMLS:C0206729 DOID:3512 GARD:0008211 Reason of obsoletion: duplicate. This will be merged with MONDO:0017827 malignant peripheral nerve sheath tumor MESH:D018319 neurofibroma