pericytic neoplasm neoplasm with perivascular epithelioid cell differentiation https://www.malacards.org/card/perivascular_epithelioid_cell_neoplasm https://www.malacards.org/card/perivascular_epithelioid_cell_tumor A soft tissue neoplasm composed of perivascular epithelioid cells. Representative examples include angiomyolipoma, clear cell-sugar-tumor of the lung, and lymphangioleiomyomatosis. tumour with perivascular epithelioid cell differentiation NCIT:C38150 Orphanet:595133 GARD:0022383 perivascular epithelioid cell tumour PEComa neoplasm with perivascular epithelioid cell differentiation MeSH definition: A family of mesenchymal tumors composed of histologically and immunohistochemically distinctive perivascular epithelioid cells. These cells do not have a normal anatomic homolog. (From Fletcher CDM, et. al., World Health Organization Classification of Tumors: Pathology and Genetics of Tumors of Soft Tissue and Bone, 2002). UMLS:C1300127 MESH:D054973 tumor with perivascular epithelioid cell differentiation MEDGEN:266246 DOID:2643 MONDO:0006359 EFO:1000464 perivascular epithelioid cell neoplasm ONCOTREE:PECOMA soft tissue neoplasm