neoplasm with perivascular epithelioid cell differentiation lymphangiomyoma MONDO:0006842 A neoplasm with perivascular epithelioid cell differentiation, often associated with tuberous sclerosis. It is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels. Sites of involvement include the lymph nodes, lung, mediastinum, and retroperitoneum. ICDO:9174/0 lymphangioleiomyoma MESH:D008203 EFO:1001027 NCIT:C3204 lymphangiomyoma GARD:0024486 UMLS:C0024223 MEDGEN:44216