has material basis in germline mutation in NLRP3 autosomal dominant disease Muckle-Wells syndrome https://www.malacards.org/card/muckle_wells_syndrome ICD9:708.8 Orphanet:575 SCTID:402417009 Muckle-Wells syndrome NCIT:C119054 MEDGEN:120634 neutrophilic urticaria GARD:0008472 MWS MedDRA:10064569 MONDO:0008633 DOID:0050854 urticaria, deafness and amyloidosis UMLS:C0268390 An intermediate form of cryopyrin-associated periodic syndrome (CAPS) and is characterized by recurrent fever (with malaise and chills), recurrent urticaria-like skin rash, sensorineural deafness, general signs of inflammation (eye redness, headaches, arthralgia/myalgia) and potentially life-threatening secondary amyloidosis (AA type). NANDO:1200467 Muckle Wells syndrome NANDO:2201067 OMIM:191900 NORD:1459 icd11.foundation:1983358487 cryopyrin-associated periodic syndrome obsolete secondary glomerular disease