has material basis in germline mutation in disease has feature WT1 Male pseudohermaphroditism Diffuse mesangial sclerosis autosomal dominant disease syndromic disease Denys-Drash syndrome https://github.com/monarch-initiative/mondo/issues/4521 https://github.com/monarch-initiative/mondo/issues/6753 https://www.malacards.org/card/denys_drash_syndrome Drash syndrome MESH:D030321 DOID:3764 Denys-Drash syndrome Wilms tumour and pseudo- or true hermaphroditism icd11.foundation:904981302 pseudohermaphroditism, nephron disorder and Wilms' tumour NCIT:C84668 ICD9:189.0 NORD:1044 Denys-Drash syndrome, autosomal dominant, somatic mutation DDS NANDO:2200116 SCTID:236385009 nephropathy associated with male pseudohermaphroditism and Wilms' tumour MedDRA:10070179 Denys-Drash syndrome (DDS) is a rare urogenital disorder characterized by the association of diffuse mesangial sclerosis (DMS), male pseudohermaphroditism with a 46,XY karyotype, and nephroblastoma. MONDO:0008682 nephropathy associated with male pseudohermaphroditism and Wilms' tumor GARD:0005576 OMIM:194080 Wilms tumour and pseudohermaphroditism Denys Drash syndrome Orphanet:220 Wilms tumor and pseudohermaphroditism UMLS:C0950121 MEDGEN:181980 nephrotic syndrome type 4 pseudohermaphroditism, nephron disorder and Wilms' tumor 46 XY differences of sex development