idiopathic interstitial pneumonia desquamative interstitial pneumonia https://github.com/monarch-initiative/mondo/issues/9097 https://www.malacards.org/card/interstitial_pneumonitis_desquamative_familial OMIM:263000 DIP MONDO:0009887 interstitial pneumonitis, desquamative, familial ICD10CM:J84.117 NANDO:1200422 NANDO:1200423 NCIT:C35288 A rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. It usually occurs in smokers. Some patients develop progressive interstitial lung fibrosis. DOID:0050158 desquamative interstitial pneumonia MESH:C562470 ICD9:516.37 RBILD GARD:0016864 icd11.foundation:1620001155 ICD9:516.34 UMLS:C0238378 respiratory bronchiolitis interstitial lung disease MEDGEN:65962 SCTID:8549006 Orphanet:98852