hereditary disease isolated right ventricular hypoplasia https://www.malacards.org/card/right_ventricular_hypoplasia_isolated right ventricular hypoplasia MONDO:0010179 right ventricular hypoplasia, isolated Irvh MEDGEN:336377 GARD:0004721 right ventricle hypoplasia Orphanet:439 SCTID:718135001 UMLS:C1848587 MESH:C535682 Isolated right ventricular hypoplasia (IRVH) is a rare congenital heart malformation characterized by underdevelopment of the right ventricle associated with patent foramen ovale or interauricular communication and normally developed tricuspid and pulmonary valves. IRVH manifests with severe cyanosis, congestive heart failure, and in severe cases, death in early infancy. OMIM:277200 isolated hypoplasia of the right ventricle hypoplasia of the right ventricle hypoplastic right heart syndrome