microtia https://www.malacards.org/card/microtia_anotia microtia, congenital microtias, congenital congenital microtias ICD10CM:Q17.2 SCTID:35045004 ICD9:744.23 icd11.foundation:2005415414 MONDO:0010920 MESH:D065817 anotia Orphanet:83463 microtia-anotia A congenital malformation of the external ear, seen more frequently in males, that occurs sporadically or is inherited, that is characterized by unilateral (79-93% of cases, 60% of which involve the right ear) or bilateral small and abnormally shaped auricles and that is often associated with atresia or stenosis of the ear canal, attention deficit disorders and delayed language development. The variation in auricle size ranges from grade I, where the auricle is simply smaller than normal, to grade IV, also known as anotia, where there is a complete absence of the external ear and of the auditory canal. GARD:0000431 UMLS:C1833486 OMIM:600674 MedDRA:10027555 MESH:C537772 M-A MEDGEN:322201 developmental defect during embryogenesis otorhinolaryngologic disease