congenital heart disease tricuspid atresia https://www.malacards.org/card/tricuspid_atresia NCIT:C85202 NANDO:1200706 tricuspid atresia (disease) tricuspid atresia (disease) DOID:0080169 NANDO:1200962 MedDRA:10049767 icd11.foundation:845891723 UMLS:C0243002 SCTID:63042009 GARD:0005274 OMIM:605067 tricuspid valve atresia NANDO:2100073 congenital atresia of tricuspid valve Tricuspid atresia is (TA) a rare congenital heart malformation characterized by the congenital agenesis of tricuspid valve leading to severe hypoplasia of right ventricle (functionally univentricular). TA is associated with normally related or transposed great vessels (TGV), an obligatory interatrial connection that is crucial for survival (patent foramen ovale or atrial septal defect, osteum secondum type), ventricular septal defect (in 90% cases), pulmonary outflow obstruction - pulmonary atresia, stenosis or hypoplasia (usually in TA with normally related vessels but also in TGV), aortic coarctation and/or aortic arch interruption (usually in TA with TGV). congenital agenesis of the tricuspid valve tricuspid atresia MEDGEN:67034 MESH:D018785 MONDO:0011514 HP:0011662 Orphanet:1209 NANDO:2200251 congenital tricuspid malformation cardiogenetic disease