bifid nose, autosomal recessive paramedian nasal cleft https://www.malacards.org/card/paramedian_nasal_cleft alar cleft ICD9:748.1 UMLS:C4759655 MEDGEN:1681273 Tessier number 1 cleft GARD:0016973 alar rim cleft Paramedian nasal cleft is a rare developmental defect during embryogenesis characterized by a unilateral or bilateral coloboma of the nose, ranging in severity from a small notch, resulting in minor deviation of the nasal septum, to variable-sized clefts of the nasal ala which may be associated with small cysts or sinuses in the nasal midline. Defect may be isolated or may occur in association with cleft lip and/or other craniofacial anomalies (e.g. hypertelorism, broadening of nasal root, midline cleft). Dorsum and apex of nose are usually well preserved. SCTID:204521002 icd11.foundation:1147502981 MONDO:0015414 cleft nose isolated cleft of the ala nasi Orphanet:141242 isolated coloboma of the nose