neurodegenerative disease infantile bilateral striatal necrosis SCTID:718174008 IBSN icd11.foundation:1947032348 striatal degeneration familial striatonigral degeneration infantile infantile striatonigral degeneration Orphanet:1576 infantile striatonigral necrosis infantile bilateral striatal necrosis UMLS:C0795996 SNDI NANDO:2200888 MONDO:0015518 Several syndromes of bilateral symmetric spongy degeneration of the caudate nucleaus, putamen and globus pallidus characterized by developmental regression, choreoathetosis and dystonia progressing to spastic quadriparesis. IBSN can be familial or sporadic. GARD:0005040 MEDGEN:167090 NANDO:2100242 obsolete rare genetic syndromic intellectual disability obsolete miscellaneous movement disorder due to neurodegenerative disease obsolete miscellaneous movement disorder due to genetic neurodegenerative disease